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INDRODUCTION
CONGENITAL HEART DISEASE OR A
CONGENITAL HEART DEFECT IS A
HEART ABNORMALITY PRESENT AT
BIRTH THE PROBLEM CAN AFFECT
 THE HEART WALLS
THE HEART VALVES
THE BLOOD VESSELS
DEFINITION
• CONGENITAL HEART DISEASE IS A
MALFORMATION OF THE HEART
,AORTA OR OTHER LARGE BLOOD
VESSELS THAT IS THE MOST
FREQUENT FROM OF MAJOR BIRTH
DEFECT IN NEWBORN
CHD – Epidemiology
• 600-700/100 000 (live newborn in CR) ~ 6-
7/1000
• 30-40% of all CHD - Ventricular Septal
Defect (VSD) - most common CHD
• Bicuspid Aortic Valve – 1-2% of General
Population
• Atrial Septal Defect – Most common CHD
diagnosed in adulthood
• No exact evidence – Complex CHD
(e.g.TGA+VSD)
PROBIEMS WITH GENES OR
CHROMOSOMES IN THE CHILD ,SUCH
AS DOWN SYNDROME
TAKING CERTAIN MRDICATION ,OR
ALCOHOL OR DRINK ABUSE DURING
PREGNANCY
A VIRAL INFECTION LIKE RUBELLA
(GERMAN MEASLES)IN THE MOTHER
IN THE FIRST TRIMESTER OF
PREGNANCY
GENERAL SIGNS
 SHORTNESS OF BREATH
 CYANOSIS
 FAINTING
 HEART MURMUR
ASSOCIATED SIGNS
VACTERL ASSOCIATION
V-VERTEBRAL ANOMALIES
A-ANAL ATRESIA
C-CARDIO VASCULAR ANOMALIES
T-TRACHEOESOPHAGEAL FISTULA
E-ESOPHAGEAL ATRESIA
R-RENAL or RADIAL ANOMALIES
L-LIMB DEFECTS
ACYANOTIC HERAT DISEASE
BLOOD IS SHUNDED FROM THE
LEFT SIDE OF THE HEART TO THE
RIGHT SIDE OF THE HEART DUE TO A
STRUCTURAL DEFECT IN THE INTER
VENTRICULAR SEPTUM
ACYANOTIC HEART DISEASE MAT
SHOW CYANOSIS(turn blue due to
insufficient oxygen in the blood)
HEART ABNORMALITY WITH LEFT
RIGHT SHUNT (ACYANOTIC WITH A LEFT
RIGHT SHUNT AN INCREASED
PULMONARY PERFUSION TO THE
DETRIMENT OF THE SYSTEMIC
CIRULATION SYSTEM IN THE RESULT
SHUNT FROM THE OXYGEN RICH SIDE
TO THE OXYGEN POOR SIDE ARE NOT
USUALLY ACCOMPANIED BY A
CYANOSIS PERSISTING DUCTUS
ARTERIOSUS(PDA)
• Left to right shunt as blood flow from aorta
•
• pulmonary over load
OUT FLOW OBSTRUCTION
A ventricular out flow tract obstraction
is one type of congenital heart defect in
which either the right or left ventricular out
flow tract is blocked or obstruction.
Introduction;
Definition;
a condition in which the
pulmonary valve is too tight so that the flow
of blood from the right ventricle of the heart
in to the pulmonary artery is impeded this
means that the right ventricle must pump
harder than normal to over come the
obstruction.
signs @ symptoms;
 heart murmur
 shortness of breath
 fainting(loss of consciousness)
 chest pain
 fatigue
Introduction;
Pathophysiology :
Increase out flow obstruction
left ventricular hypertrophy
increase left ventricular end diastolic volume
increase pulmonary capillary pressure
pulmonary edema
diastolic heart failure
AS
COARCTATION OF AORDA:
TOF:Introduction
Definition:
TOF is a type of heart defect
present at birth stmtoms include episodes of
bluish colour to the skin other symtoms may
include a heart murmur finger clubbing and
easy tiring upon breast feeding
CAUSES:
PATHOPHYSIOLOGY:
Right ventricular hypertrophy with out
cardiac enlargement and increase in right
ventricular pressure
Right to left shuunt appars to decompress
the right ventricle
VSD is silent
Ejection systolic murmur
pulmonic stenosis
TOF
CLINICAL MANIFESTRATION:
CYANOSIS
BREATHING DIFFICULTY
HEART MURMUR
FINGER CLUBBING
TGA
Thank you for your attention!!!

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Congenital heart diseases

  • 1.
  • 2. INDRODUCTION CONGENITAL HEART DISEASE OR A CONGENITAL HEART DEFECT IS A HEART ABNORMALITY PRESENT AT BIRTH THE PROBLEM CAN AFFECT  THE HEART WALLS THE HEART VALVES THE BLOOD VESSELS
  • 3. DEFINITION • CONGENITAL HEART DISEASE IS A MALFORMATION OF THE HEART ,AORTA OR OTHER LARGE BLOOD VESSELS THAT IS THE MOST FREQUENT FROM OF MAJOR BIRTH DEFECT IN NEWBORN
  • 4. CHD – Epidemiology • 600-700/100 000 (live newborn in CR) ~ 6- 7/1000 • 30-40% of all CHD - Ventricular Septal Defect (VSD) - most common CHD • Bicuspid Aortic Valve – 1-2% of General Population • Atrial Septal Defect – Most common CHD diagnosed in adulthood • No exact evidence – Complex CHD (e.g.TGA+VSD)
  • 5. PROBIEMS WITH GENES OR CHROMOSOMES IN THE CHILD ,SUCH AS DOWN SYNDROME TAKING CERTAIN MRDICATION ,OR ALCOHOL OR DRINK ABUSE DURING PREGNANCY A VIRAL INFECTION LIKE RUBELLA (GERMAN MEASLES)IN THE MOTHER IN THE FIRST TRIMESTER OF PREGNANCY
  • 6. GENERAL SIGNS  SHORTNESS OF BREATH  CYANOSIS  FAINTING  HEART MURMUR
  • 7. ASSOCIATED SIGNS VACTERL ASSOCIATION V-VERTEBRAL ANOMALIES A-ANAL ATRESIA C-CARDIO VASCULAR ANOMALIES T-TRACHEOESOPHAGEAL FISTULA E-ESOPHAGEAL ATRESIA R-RENAL or RADIAL ANOMALIES L-LIMB DEFECTS
  • 8.
  • 9. ACYANOTIC HERAT DISEASE BLOOD IS SHUNDED FROM THE LEFT SIDE OF THE HEART TO THE RIGHT SIDE OF THE HEART DUE TO A STRUCTURAL DEFECT IN THE INTER VENTRICULAR SEPTUM ACYANOTIC HEART DISEASE MAT SHOW CYANOSIS(turn blue due to insufficient oxygen in the blood)
  • 10. HEART ABNORMALITY WITH LEFT RIGHT SHUNT (ACYANOTIC WITH A LEFT RIGHT SHUNT AN INCREASED PULMONARY PERFUSION TO THE DETRIMENT OF THE SYSTEMIC CIRULATION SYSTEM IN THE RESULT SHUNT FROM THE OXYGEN RICH SIDE TO THE OXYGEN POOR SIDE ARE NOT USUALLY ACCOMPANIED BY A CYANOSIS PERSISTING DUCTUS ARTERIOSUS(PDA)
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  • 27. • Left to right shunt as blood flow from aorta • • pulmonary over load
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  • 41. OUT FLOW OBSTRUCTION A ventricular out flow tract obstraction is one type of congenital heart defect in which either the right or left ventricular out flow tract is blocked or obstruction.
  • 43. Definition; a condition in which the pulmonary valve is too tight so that the flow of blood from the right ventricle of the heart in to the pulmonary artery is impeded this means that the right ventricle must pump harder than normal to over come the obstruction.
  • 44. signs @ symptoms;  heart murmur  shortness of breath  fainting(loss of consciousness)  chest pain  fatigue
  • 45.
  • 46.
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  • 49.
  • 50.
  • 51. Pathophysiology : Increase out flow obstruction left ventricular hypertrophy increase left ventricular end diastolic volume increase pulmonary capillary pressure pulmonary edema diastolic heart failure AS
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  • 72.
  • 73.
  • 75. Definition: TOF is a type of heart defect present at birth stmtoms include episodes of bluish colour to the skin other symtoms may include a heart murmur finger clubbing and easy tiring upon breast feeding
  • 77. PATHOPHYSIOLOGY: Right ventricular hypertrophy with out cardiac enlargement and increase in right ventricular pressure Right to left shuunt appars to decompress the right ventricle VSD is silent
  • 80.
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  • 87. TGA
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  • 101. Thank you for your attention!!!