2. Intoduction
• Epidermoid cysts generally presents as soft, freely movable,
slowly enlarging, nontender masses, most commonly in the
supero-temporal periorbital margin.
• These are the most common orbital neoplasms in the pediatric
age group, a majority of them presenting within the first decade
of life.
• These tumors are basically choristomas and results from
sequestration of surface ectoderm at bone suture lines or along
the lines of embryonic closure.[1]
• Epidermoid cyst contains stratified squamous epithelium
forming the wall of the cyst.
• The lesions often connect to bone sutures by way of fibrous
attachments. The frontal–zygomatic suture is the most common
attachment for the periorbital epidermoid.
• Although the supero-temporal quadrant is the most
characteristic location, these lesions may occur in any
periorbital location.
3. Introduction
• These tumors are likely to remodel the orbital walls or rim
due to pressure effects, which may lead to fossa formation
in orbital wall.
• Occasionally these tumors may extend into the temporal
fossa or even into intracranial space due to extensive bone
erosion. [2]
• Signs and symptoms depends upon the location of the
tumor (periorbital or orbital tumors).
• Periorbital tumors are cosmetically unappealing while
orbital tumors may present with diplopia and proptosis.[3]
• Another presentation of these tumors consists of orbital
inflammation after blunt trauma. In this situation, trauma
results in the rupture of the cyst, with the release of its
contents into the soft tissues. Inflammatory foreign body
reaction ensues.
4. Case Report
• A five year old female child presented with a soft, non-
tender, freely movable, non-pulsatile, non reducible
swelling, which was present since birth, over the left
supero-temporal orbital margin.
• The swelling was smaller at birth, but it gradually
increased to present size, within the course of five years.
5. Clinical Features
• Size of the tumor is 5 x 5 x 2.5 cm.
• Tumor has smooth surface with well defined
margins.
• Fluctuation test is positive.
• Trans-illumination test is negative.
• Temperature not raised as compared to contralateral
side.
• No pus-point, scar-mark or dialated blood vessels
present over the swelling.
• No history of discharge from the swelling.
• No palpable regional lymph nodes are felt.
• No similar swelling present over rest of the body.
6. Treatment
• A horizantal incision made on the skin over the swelling and the
tumor exposed.
• Blunt dissecction done around the tumor and intact lump was
excised.
9. Post operative results
• The swelling subsided after the tumor excision.
• Skin sutures were removed on eighth post-
operative day.
10. Conclusion
• Although peri-orbital epiermoid cysts are
usually painless, they impart a cosmetically
challanged appearance.
• As there is no medical line of management of
these tumors, they are to be managed
surgically.
11. Refrences
1. Gary E. Borodic; Principles and Practice of Ophthalmology,
Chapter 228, Cystic Lesions of the Orbit; Third Edition : 2903-
2912.
2. Grove AS: Giant dermoid cyst of the orbit. Ophthalmology
1979; 86:1513–1520.
3. Rootman J: Diseases of the orbit. Philadelphia: JB Lippincott;
1988:489.